Search Ontology:
ChEBI
(2R,3S)-2-hydroxy-3-methylpentanoic acid
- Term ID
- CHEBI:55536
- Synonyms
-
- (2R,3S)-2-hydroxy-3-methylpentanoic acid
- (2R,3S)-2-hydroxy-3-methylvaleric acid
- (2R,3S)-HMVA
- (2R,3S)-isoleucic acid
- (R,S)-isoleucic acid
- HMVA
- Definition
- A valeric acid derivative having an (R)-hydroxy substituent at the 2-position and an (S)-methyl substituent at the 3-position; one of 4 steroisomers of 2-hydroxy-3-methylpentanoic acid, generated by isoleucine metabolism. Found at significantly higher levels than normal in patients with maple syrup urine disease (MSUD).
- References
-
- Beilstein:1721800
- PMID:1429566
- Ontology
- ChEBI ( EBI )
- is a type of
-
- has_functional_parent
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- inverse is_conjugate_base_of
-
- is_conjugate_acid_of
-
Show first 5 Terms
Phenotype
Phenotype resulting from (2R,3S)-2-hydroxy-3-methylpentanoic acid
Phenotype where environments contain (2R,3S)-2-hydroxy-3-methylpentanoic acid
Phenotype modified by environments containing (2R,3S)-2-hydroxy-3-methylpentanoic acid
Human Disease Model