Term Name: | lymphangiomyomatosis |
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Synonyms: | Lymphangioleiomyomatosis. |
Definition: | Characterized by benign peribronchial, perivascular, and perilymphatic proliferation of atypical smooth muscle resulting in vascular and airway obstruction, cyst formation, and a progressive decline in lung function. (M- 9174/1). |
Ontology: | MPATH [MPATH:421] |