Term Name:	progressive pseudorheumatoid arthropathy of childhood
Synonyms:	spondyloepiphyseal dysplasia tarda-progressive arthropathy syndrome
Definition:	A osteochondrodysplasia characterized by autosomal recessive inheritance with typical onset around 3 years of age, progressive severe degenerative joint disease, platyspondyly, epiphyseal enlargement but absence of inflammatory joint disease that has_material_basis_in homozygous or compound heterozygous mutation in the CHST3 gene on chromosome 10q22.
Ontology:	Human Disease [DOID:0090004]   ( DOID:0090004 )