Term Name:	nephrotic syndrome type 7
Synonyms:	Ig-mediated membranoproliferative glomerulonephritis, Ig-mediated MPGN, immunoglobulin-mediated membranoproliferative glomerulonephritis, Immunoglobulin-mediated MPGN, nephrotic syndrome type 7 with membranoptoliferative glomerulonephritis
Definition:	A familial nephrotic syndrome characterized by onset in the first decade of life of progressive renal disease with proteinuria and membranoproliferative glomerulonephritis that has_material_basis_in homozygous or compound heterozygous mutation in the DGKE gene on chromosome 17q22.
Ontology:	Human Disease [DOID:0080388]   ( DOID:0080388 )