Term Name: (2R,3S)-2-hydroxy-3-methylpentanoic acid
Synonyms: (2R,3S)-2-hydroxy-3-methylpentanoic acid, (2R,3S)-2-hydroxy-3-methylvaleric acid, (2R,3S)-HMVA, (2R,3S)-isoleucic acid, (R,S)-isoleucic acid, HMVA
Definition: A valeric acid derivative having an (R)-hydroxy substituent at the 2-position and an (S)-methyl substituent at the 3-position; one of 4 steroisomers of 2-hydroxy-3-methylpentanoic acid, generated by isoleucine metabolism. Found at significantly higher levels than normal in patients with maple syrup urine disease (MSUD).
Ontology: ChEBI [CHEBI:55536]  ( EBI )

Relationships
is a type of: (2R)-2-hydroxy monocarboxylic acid 2-hydroxy-3-methylpentanoic acid
has_functional_parent: valeric acid
inverse is_conjugate_base_of: (2R,3S)-2-hydroxy-3-methylpentanoate
is_conjugate_acid_of: (2R,3S)-2-hydroxy-3-methylpentanoate