Term Name: (R)-2-hydroxy-4-methylpentanoic acid
Synonyms: (2R)-2-hydroxy-4-methylpentanoic acid, (R)-2-hydroxy-4-methylpentanoic acid, (R)-2-hydroxy-4-methylvaleric acid, (R)-2-hydroxyisocaproic acid, (R)-leucic acid, 2-hydroxy-4-methyl-D-valeric acid, alpha-Hydroxyisocaproic acid, D-2-hydroxy-4-methylpentanoic acid, D-2-hydroxy-4-methylvaleric acid, D-2-hydroxyisocaproic acid, D-leucic acid, delta-leucic acid, leucic acid
Definition: The (R)-enantiomer of 2-hydroxy-4-methylpentanoic acid. Found in patients with short-bowel syndrome (an inborn error of metabolism), and in maple syrup urine disease, MSUD.
Ontology: ChEBI [CHEBI:55534]  ( EBI )

Relationships
is a type of: (2R)-2-hydroxy monocarboxylic acid 2-hydroxy-4-methylvaleric acid
inverse has_functional_parent: (R)-2-hydroxy-4-methylpentanoyl-CoA
inverse is_conjugate_base_of: (R)-2-hydroxy-4-methylpentanoate
inverse is_enantiomer_of: (S)-2-hydroxy-4-methylpentanoic acid
is_conjugate_acid_of: (R)-2-hydroxy-4-methylpentanoate
is_enantiomer_of: (S)-2-hydroxy-4-methylpentanoic acid